ORF gene description subcellular functional category funcat description Q0045 COX1 CYTOCHROME-C OXIDASE SUBUNIT I mitochondrial inner membrane [E] COX1 cytochrome-c oxidase subunit I Q0070 AI5_ALPHA DNA ENDONUCLEASE AI5_ALPHA mitochondria [U] AI5_ALPHA DNA endonuclease AI5_ALPHA Q0085 ATP6 F1F0-ATPASE COMPLEX,FO A SUBUNIT mitochondrial inner membrane [E] ATP6 F1F0-ATPase complex, FO A subunit Q0250 COX2 CYTOCHROME-C OXIDASE SUBUNIT II mitochondrial inner membrane [E] COX2 cytochrome-c oxidase subunit II YAL039C CYC3 HOLOCYTOCHROME-C SYNTHASE (CYTOCHROME C HEME LYASE) mitochondrial intermembrane space [F] CYC3 holocytochrome-c synthase (cytochrome c heme lyase) YBL045C COR1 UBIQUINOL--CYTOCHROME-C REDUCTASE 44K CORE PROTEIN mitochondrial inner membrane [E] COR1 ubiquinol--cytochrome-c reductase 44K core protein YBL064C STRONG SIMILARITY TO THIOL-SPECIFIC ANTIOXIDANT ENZYME mitochondrial matrix [R] YBL064c strong similarity to thiol-specific antioxidant enzyme YBL080C PET112 REQUIRED TO MAINTAIN RHO+ MITOCHONDRIAL DNA mitochondria [P] PET112 required to maintain rho+ mitochondrial DNA YBL099W ATP1 F1F0-ATPASE COMPLEX,F1 ALPHA SUBUNIT mitochondrial inner membrane [E] ATP1 F1F0-ATPase complex, F1 alpha subunit YBR037C SCO1 INVOLVED IN STABILIZATION OF COX1P AND COX2P mitochondrial inner membrane [F] SCO1 involved in stabilization of COX1P and COX2P YBR039W ATP3 F1F0-ATPASE COMPLEX,F1 GAMMA SUBUNIT mitochondrial inner membrane [E] ATP3 F1F0-ATPase complex, F1 gamma subunit YBR084W MIS1 C1-TETRAHYDROFOLATE SYNTHASE PRECURSOR,MITOCHONDRIAL mitochondria [G] MIS1 C1-tetrahydrofolate synthase precursor, mitochondrial YBR085W AAC3 ADP/ATP CARRIER PROTEIN (MCF) mitochondrial inner membrane [O] AAC3 ADP/ATP carrier protein (MCF) YBR122C MRPL36 RIBOSOMAL PROTEIN YML36 PRECURSOR,MITOCHONDRIAL mitochondrial matrix [P] MRPL36 ribosomal protein YmL36 precursor, mitochondrial YBR192W RIM2 MITOCHONDRIAL CARRIER PROTEIN (MCF) mitochondrial inner membrane [E] RIM2 mitochondrial carrier protein (MCF) YBR221C PDB1 PYRUVATE DEHYDROGENASE (LIPOAMIDE) BETA CHAIN PRECURSOR mitochondrial matrix [E] PDB1 pyruvate dehydrogenase (lipoamide) beta chain precursor YBR227C MCX1 SIMILARITY TO E.COLI ATP-BINDING PROTEIN CLPX mitochondrial matrix [F] MCX1 similarity to E.coli ATP-binding protein clpX YBR263W SHM1 SERINE HYDROXYMETHYLTRANSFERASE PRECURSOR,MITOCHONDRIAL mitochondria [M] SHM1 serine hydroxymethyltransferase precursor, mitochondrial YBR282W MRPL27 RIBOSOMAL PROTEIN YML27 PRECURSOR,MITOCHONDRIAL mitochondrial matrix [P] MRPL27 ribosomal protein YmL27 precursor, mitochondrial YCL009C ILV6 ACETOLACTATE SYNTHASE,REGULATORY SUBUNIT mitochondria [G] ILV6 acetolactate synthase, regulatory subunit YCL064C CHA1 L-SERINE/L-THREONINE DEAMINASE mitochondria [G] CHA1 L-serine/L-threonine deaminase YDL004W ATP16 F1F0-ATPASE COMPLEX,F1 DELTA SUBUNIT mitochondrial inner membrane [E] ATP16 F1F0-ATPase complex, F1 delta subunit YDL066W IDP1 ISOCITRATE DEHYDROGENASE (NADP+),MITOCHONDRIAL mitochondria [E] IDP1 isocitrate dehydrogenase (NADP+), mitochondrial YDL174C DLD1 D-LACTATE FERRICYTOCHROME C OXIDOREDUCTASE (D-LCR) mitochondrial inner membrane [E] DLD1 D-lactate ferricytochrome C oxidoreductase (D-LCR) YDL198C YHM1 MEMBER OF THE MITOCHONDRIAL CARRIER FAMILY (MCF) mitochondrial inner membrane [A] YHM1 member of the mitochondrial carrier family (MCF) YDR019C GCV1 GLYCINE DECARBOXYLASE,SUBUNIT T mitochondrial matrix [G] GCV1 glycine decarboxylase, subunit T YDR148C KGD2 2-OXOGLUTARATE DEHYDROGENASE COMPLEX E2 COMPONENT mitochondrial matrix [E] KGD2 2-oxoglutarate dehydrogenase complex E2 component YDR178W SDH4 SUCCINATE DEHYDROGENASE MEMBRANE ANCHOR SUBUNIT FOR SDH2P mitochondrial inner membrane [E] SDH4 succinate dehydrogenase membrane anchor subunit for SDH2P YDR197W CBS2 CYTOCHROME B TRANSLATIONAL ACTIVATOR PROTEIN mitochondrial inner membrane [P] CBS2 cytochrome B translational activator protein YDR232W HEM1 5-AMINOLEVULINATE SYNTHASE mitochondrial matrix [M] HEM1 5-aminolevulinate synthase YDR258C HSP78 HEAT SHOCK PROTEIN OF CLPB FAMILY OF ATP-DEPENDENT PROTEASES,MITOCHONDRIAL mitochondrial matrix [F] HSP78 heat shock protein of clpb family of ATP-dependent proteases, mitochondrial YDR298C ATP5 F1F0-ATPASE COMPLEX,OSCP SUBUNIT mitochondrial inner membrane [E] ATP5 F1F0-ATPase complex, OSCP subunit YDR337W MRPS28 RIBOSOMAL PROTEIN OF THE SMALL SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPS28 ribosomal protein of the small subunit, mitochondrial YDR375C BCS1 MITOCHONDRIAL PROTEIN OF THE CDC48/PAS1/SEC18 (AAA) FAMILY OF ATPASES mitochondrial inner membrane [F] BCS1 mitochondrial protein of the CDC48/PAS1/SEC18 (AAA) family of ATPases YDR376W ARH1 MITOCHONDRIAL PROTEIN WITH SIMILARITY TO HUMAN ADRENODOXIN REDUCTASE AND FERREDOXIN-NADP+ REDUCTASE mitochondrial inner membrane [M] ARH1 mitochondrial protein with similarity to human adrenodoxin reductase and ferredoxin-NADP+ reductase YDR377W ATP17 ATP SYNTHASE COMPLEX,SUBUNIT F mitochondrial inner membrane [E] ATP17 ATP synthase complex, subunit f YDR405W MRP20 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRP20 ribosomal protein of the large subunit, mitochondrial YDR529C QCR7 UBIQUINOL--CYTOCHROME-C REDUCTASE SUBUNIT 7 mitochondrial inner membrane [E] QCR7 ubiquinol--cytochrome-c reductase subunit 7 YEL024W RIP1 UBIQUINOL--CYTOCHROME-C REDUCTASE IRON-SULFUR PROTEIN PRECURSOR mitochondrial inner membrane [E] RIP1 ubiquinol--cytochrome-c reductase iron-sulfur protein precursor YEL030W ECM10 HEAT SHOCK PROTEIN OF HSP70 FAMILY mitochondrial matrix [F] ECM10 heat shock protein of HSP70 family YEL039C CYC7 CYTOCHROME-C ISOFORM 2 mitochondrial intermembrane space [E] CYC7 cytochrome-c isoform 2 YER014W HEM14 PROTOPORPHYRINOGEN OXIDASE,MITOCHONDRIAL mitochondrial inner membrane [M] HEM14 protoporphyrinogen oxidase, mitochondrial YER017C AFG3 PROTEASE OF THE SEC18/CDC48/PAS1 FAMILY OF ATPASES (AAA) mitochondrial inner membrane [F] AFG3 protease of the SEC18/CDC48/PAS1 family of ATPases (AAA) YER024W YAT2 CARNITINE O-ACETYLTRANSFERASE mitochondria [M] YAT2 carnitine O-acetyltransferase YER073W ALD5 ALDEHYDE DEHYDROGENASE (NAD+),MITOCHONDRIAL mitochondria [E] ALD5 aldehyde dehydrogenase (NAD+), mitochondrial YER086W ILV1 ANABOLIC SERINE AND THREONINE DEHYDRATASE PRECURSOR mitochondria [G] ILV1 anabolic serine and threonine dehydratase precursor YER141W COX15 CYTOCHROME OXIDASE ASSEMBLY FACTOR mitochondrial inner membrane [E] COX15 cytochrome oxidase assembly factor YER154W OXA1 CYTOCHROME OXIDASE BIOGENESIS PROTEIN mitochondrial inner membrane [F] OXA1 cytochrome oxidase biogenesis protein YFL016C MDJ1 HEAT SHOCK PROTEIN - CHAPERONE mitochondrial inner membrane [F] MDJ1 heat shock protein - chaperone YFL018C LPD1 DIHYDROLIPOAMIDE DEHYDROGENASE PRECURSOR mitochondrial matrix [G] LPD1 dihydrolipoamide dehydrogenase precursor YGL187C COX4 CYTOCHROME-C OXIDASE CHAIN IV mitochondrial inner membrane [E] COX4 cytochrome-c oxidase chain IV YGL191W COX13 CYTOCHROME-C OXIDASE CHAIN VIA mitochondrial inner membrane [E] COX13 cytochrome-c oxidase chain VIa YGL236C MTO1 STRONG SIMILARITY TO GIDA E.COLI PROTEIN mitochondrial matrix [P] MTO1 strong similarity to gidA E.coli protein YGR076C MRPL25 RIBOSOMAL PROTEIN YML25,MITOCHONDRIAL mitochondrial matrix [P] MRPL25 ribosomal protein YmL25, mitochondrial YGR082W TOM20 MITOCHONDRIAL OUTER MEMBRANE IMPORT RECEPTOR SUBUNIT, 20 KD mitochondrial outer membrane [O] TOM20 mitochondrial outer membrane import receptor subunit, 20 kD YGR132C PHB1 PROHIBITIN,ANTIPROLIFERATIVE PROTEIN mitochondrial inner membrane [D] PHB1 prohibitin, antiproliferative protein YGR207C ELECTRON-TRANSFERRING FLAVOPROTEIN,BETA CHAIN mitochondria [E] ETF-BETA electron-transferring flavoprotein, beta chain YGR215W RSM27 STRONG SIMILARITY TO HYPOTHETICAL S. POMBE PROTEIN mitochondrial matrix [U] RSM27 strong similarity to hypothetical S. pombe protein YGR231C PHB2 PROHIBITIN mitochondrial inner membrane [D] PHB2 Prohibitin YGR244C LSC2 SUCCINATE-COA LIGASE BETA SUBUNIT mitochondrial matrix [E] LSC2 succinate-CoA ligase beta subunit YHR008C SOD2 SUPEROXIDE DISMUTASE (MN) PRECURSOR,MITOCHONDRIAL mitochondrial matrix [R] SOD2 superoxide dismutase (Mn) precursor, mitochondrial YHR024C MAS2 PROCESSING PEPTIDASE,CATALYTIC 53KDA (ALPHA) SUBUNIT,MITOCHONDRIAL mitochondrial matrix [F] MAS2 processing peptidase, catalytic 53kDa (alpha) subunit, mitochondrial YHR051W COX6 CYTOCHROME-C OXIDASE SUBUNIT VI mitochondrial inner membrane [E] COX6 cytochrome-c oxidase subunit VI YHR117W TOM71 PROTEIN WITH SIMILARITY TO TOM70P/MAS70P mitochondrial outer membrane [O] TOM71 protein with similarity to TOM70P/Mas70p YHR120W MSH1 DNA MISMATCH REPAIR PROTEIN,MITOCHONDRIAL mitochondrial matrix [D] MSH1 DNA mismatch repair protein, mitochondrial YHR147C MRPL6 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL6 ribosomal protein of the large subunit, mitochondrial YHR208W BAT1 BRANCHED CHAIN AMINO ACID AMINOTRANSFERASE,MITOCHONDRIAL mitochondrial matrix [G] BAT1 branched chain amino acid aminotransferase, mitochondrial YIL022W TIM44 MITOCHONDRIAL INNER MEMBRANE IMPORT RECEPTOR SUBUNIT mitochondrial matrix [O] TIM44 mitochondrial inner membrane import receptor subunit YIL051C MMD1 REQUIRED FOR MAINTENANCE OF MITOCHONDRIAL DNA mitochondrial matrix [C] MMF1 required for maintenance of mitochondrial DNA YIL093C RSM25 WEAK SIMILARITY TO S.POMBE HYPOTHETICAL PROTEIN SPBC16A3 mitochondrial matrix [U] RSM25 weak similarity to S.pombe hypothetical protein SPBC16A3 YIL111W COX5B CYTOCHROME-C OXIDASE CHAIN VB mitochondrial inner membrane [E] COX5B cytochrome-c oxidase chain Vb YIL125W KGD1 2-OXOGLUTARATE DEHYDROGENASE COMPLEX E1 COMPONENT mitochondrial matrix [E] KGD1 2-oxoglutarate dehydrogenase complex E1 component YIL136W OM45 PROTEIN OF THE OUTER MITOCHONDRIAL MEMBRANE mitochondrial outer membrane - - YIL155C GUT2 GLYCEROL-3-PHOSPHATE DEHYDROGENASE,MITOCHONDRIAL mitochondrial inner membrane [M] GUT2 glycerol-3-phosphate dehydrogenase, mitochondrial YIR021W MRS1 INVOLVED IN MITOCHONDRIAL RNA SPLICING OF COB MRNA mitochondria [T] MRS1 involved in mitochondrial RNA splicing of COB mRNA YJL096W MRPL49 RIBOSOMAL PROTEIN YML49,MITOCHONDRIAL mitochondrial matrix [P] MRPL49 ribosomal protein YmL49, mitochondrial YJL166W QCR8 UBIQUINOL--CYTOCHROME-C REDUCTASE CHAIN VIII mitochondrial inner membrane [E] QCR8 ubiquinol--cytochrome-c reductase chain VIII YJL180C ATP12 F1F0-ATPASE COMPLEX ASSEMBLY PROTEIN mitochondrial matrix [F] ATP12 F1F0-ATPase complex assembly protein YJL208C NUC1 NUCLEASE,MITOCHONDRIAL mitochondrial inner membrane [M] NUC1 nuclease, mitochondrial YJR016C ILV3 DIHYDROXY-ACID DEHYDRATASE mitochondria [G] ILV3 dihydroxy-acid dehydratase YJR045C SSC1 MITOCHONDRIAL HEAT SHOCK PROTEIN 70-RELATED PROTEIN mitochondrial matrix [F] SSC1 mitochondrial heat shock protein 70-related protein YJR051W OSM1 OSMOTIC GROWTH PROTEIN mitochondrial matrix [R] OSM1 osmotic growth protein YJR077C MIR1 PHOSPHATE TRANSPORT PROTEIN,MITOCHONDRIAL (MCF) mitochondrial inner membrane [O] MIR1 phosphate transport protein, mitochondrial (MCF) YJR113C RSM7 SIMILARITY TO BACTERIAL,CHLOROPLAST AND MITOCHONDRIAL RIBOSOMAL PROTEIN S7 mitochondrial matrix [P] RSM7 similarity to bacterial, chloroplast and mitochondrial ribosomal protein S7 YJR121W ATP2 F1F0-ATPASE COMPLEX,F1 BETA SUBUNIT mitochondrial inner membrane [E] ATP2 F1F0-ATPase complex, F1 beta subunit YKL016C ATP7 F1F0-ATPASE COMPLEX,FO D SUBUNIT mitochondrial inner membrane [E] ATP7 F1F0-ATPase complex, FO D subunit YKL029C MAE1 MALIC ENZYME mitochondria [M] MAE1 malic enzyme YKL040C NFU1 IRON HOMEOSTASIS mitochondrial matrix [M] NFU1 iron homeostasis YKL085W MDH1 MALATE DEHYDROGENASE PRECURSOR,MITOCHONDRIAL mitochondrial matrix [E] MDH1 malate dehydrogenase precursor, mitochondrial YKL120W OAC1 SIMILARITY TO MITOCHONDRIAL UNCOUPLING PROTEINS (MCF) mitochondrial inner membrane [O] OAC1 similarity to mitochondrial uncoupling proteins (MCF) YKL134C 36433 MITOCHONDRIAL INTERMEDIATE PEPTIDASE mitochondrial matrix [F] OCT1 mitochondrial intermediate peptidase YKL141W SDH3 CYTOCHROME B560 SUBUNIT OF RESPIRATORY COMPLEX II mitochondrial inner membrane [E] SDH3 cytochrome b560 subunit of respiratory complex II YKL148C SDH1 SUCCINATE DEHYDROGENASE FLAVOPROTEIN PRECURSOR mitochondrial inner membrane [E] SDH1 succinate dehydrogenase flavoprotein precursor YKL150W MCR1 CYTOCHROME-B5 REDUCTASE mitochondrial intermembrane space [E] MCR1 cytochrome-b5 reductase YKR066C CCP1 CYTOCHROME-C PEROXIDASE PRECURSOR mitochondrial intermembrane space [R] CCP1 cytochrome-c peroxidase precursor YLL041C SDH2 SUCCINATE DEHYDROGENASE IRON-SULFUR PROTEIN SUBUNIT mitochondrial inner membrane [E] SDH2 succinate dehydrogenase iron-sulfur protein subunit YLR069C MEF1 TRANSLATION ELONGATION FACTOR G,MITOCHONDRIAL mitochondria [P] MEF1 translation elongation factor G, mitochondrial YLR163C MAS1 MITOCHONDRIAL PROCESSING PEPTIDASE mitochondrial matrix [F] MAS1 mitochondrial processing peptidase YLR188W MDL1 ATP-BINDING CASSETTE TRANSPORTER FAMILY MEMBER mitochondrial inner membrane [A] MDL1 ATP-binding cassette transporter family member YLR259C HSP60 HEAT SHOCK PROTEIN - CHAPERONE,MITOCHONDRIAL mitochondrial matrix [F] HSP60 heat shock protein - chaperone, mitochondrial YLR355C ILV5 KETOL-ACID REDUCTO-ISOMERASE mitochondria [G] ILV5 ketol-acid reducto-isomerase YLR395C COX8 CYTOCHROME-C OXIDASE CHAIN VIII mitochondrial inner membrane [E] COX8 cytochrome-c oxidase chain VIII YML054C CYB2 LACTATE DEHYDROGENASE CYTOCHROME B2 mitochondrial intermembrane space [E] CYB2 lactate dehydrogenase cytochrome b2 YML081C-A ATP18 GENE FOR SUBUNIT I/J OF THE MITOCHONDRIAL F1F0-ATP SYNTHASE mitochondrial inner membrane [E] ATP18 gene for subunit i/j of the mitochondrial F1F0-ATP synthase YML091C RPM2 RIBONUCLEASE P PRECURSOR,MITOCHONDRIAL mitochondria [T] RPM2 ribonuclease P precursor, mitochondrial YML120C NDI1 NADH-UBIQUINONE-6 OXIDOREDUCTASE mitochondrial inner membrane [E] NDI1 NADH-ubiquinone-6 oxidoreductase YML129C COX14 CYTOCHROME-C OXIDASE ASSEMBLY PROTEIN mitochondrial inner membrane [E] COX14 cytochrome-c oxidase assembly protein YMR056C AAC1 ADP/ATP CARRIER PROTEIN (MCF) mitochondrial inner membrane [O] AAC1 ADP/ATP carrier protein (MCF) YMR062C ECM40 ACETYLORNITHINE ACETYLTRANSFERASE mitochondrial matrix [G] ECM40 acetylornithine acetyltransferase YMR072W ABF2 HIGH MOBILITY GROUP PROTEIN mitochondrial matrix [D] ABF2 high mobility group protein YMR083W ADH3 ALCOHOL DEHYDROGENASE III mitochondrial matrix [M] ADH3 alcohol dehydrogenase III YMR089C YTA12 PROTEASE OF THE SEC18/CDC48/PAS1 FAMILY OF ATPASES (AAA) mitochondrial inner membrane [F] YTA12 protease of the SEC18/CDC48/PAS1 family of ATPases (AAA) YMR108W ILV2 ACETOLACTATE SYNTHASE mitochondria [G] ILV2 acetolactate synthase YMR145C MITOCHONDRIAL CYTOSOLICALLY DIRECTED NADH DEHYDROGENASE mitochondrial inner membrane [E] NDH1 mitochondrial cytosolically directed NADH dehydrogenase YMR203W TOM40 FORMS THE HYDROPHILIC CHANNEL OF THE MITOCHONDRIAL IMPORT PORE FOR PREPROTEINS mitochondrial outer membrane [O] TOM40 forms the hydrophilic channel of the mitochondrial import pore for preproteins YMR228W MTF1 RNA POLYMERASE SPECIFIC FACTOR,MITOCHONDRIAL mitochondrial matrix [T] MTF1 RNA polymerase specific factor, mitochondrial YMR256C COX7 CYTOCHROME-C OXIDASE,SUBUNIT VII mitochondrial inner membrane [E] COX7 cytochrome-c oxidase, subunit VII YMR286W MRPL33 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL33 ribosomal protein of the large subunit, mitochondrial YMR287C MSU1 3'-5' EXONUCLEASE FOR RNA 3' SS-TAIL,MITOCHONDRIAL mitochondrial matrix [T] MSU1 3'-5' exonuclease for RNA 3' ss-tail, mitochondrial YMR301C ATM1 ATP-BINDING CASSETTE TRANSPORTER PROTEIN,MITOCHONDRIAL mitochondrial inner membrane [O] ATM1 ATP-binding cassette transporter protein, mitochondrial YNL005C MRP7 RIBOSOMAL PROTEIN YML2 PRECURSOR,MITOCHONDRIAL mitochondrial matrix [P] MRP7 ribosomal protein YmL2 precursor, mitochondrial YNL037C IDH1 ISOCITRATE DEHYDROGENASE (NAD+) SUBUNIT 1,MITOCHONDRIAL mitochondrial matrix [E] IDH1 isocitrate dehydrogenase (NAD+) subunit 1, mitochondrial YNL052W COX5A CYTOCHROME-C OXIDASE CHAIN V.A PRECURSOR mitochondrial inner membrane [E] COX5A cytochrome-c oxidase chain V.A precursor YNL070W TOM7 MITOCHONDRIAL OUTER MEMBRANE IMPORT RECEPTOR SUBUNIT,7 KD mitochondrial outer membrane [O] TOM7 mitochondrial outer membrane import receptor subunit, 7 kD YNL071W LAT1 DIHYDROLIPOAMIDE S-ACETYLTRANSFERASE mitochondrial matrix [E] LAT1 dihydrolipoamide S-acetyltransferase YNL121C TOM70 MITOCHONDRIAL OUTER MEMBRANE SPECIALIZED IMPORT RECEPTOR mitochondrial outer membrane [A] TOM70 mitochondrial outer membrane specialized import receptor YNL131W TOM22 MITOCHONDRIAL OUTER MEMBRANE IMPORT RECEPTOR COMPLEX SUBUNIT mitochondrial outer membrane [A] TOM22 mitochondrial outer membrane import receptor complex subunit YNL185C MRPL19 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL19 ribosomal protein of the large subunit, mitochondrial YNL256W FOL1 DIHYDRONEOPTERIN ALDOLASE,DIHYDRO-6-HYDROXYMETHYLPTERIN PYROPHOSPHOKINASE,DIHYDROPTEROATE SYNTHETASE mitochondria [M] FOL1 Dihydroneopterin aldolase, dihydro-6-hydroxymethylpterin pyrophosphokinase, dihydropteroate synthetase YNL284C MRPL10 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL10 ribosomal protein of the large subunit, mitochondrial YNL328C MDJ2 HEAT SHOCK PROTEIN - CHAPERONE mitochondrial inner membrane [F] MDJ2 heat shock protein - chaperone YNR001C CIT1 CITRATE (SI)-SYNTHASE,MITOCHONDRIAL mitochondrial matrix [E] CIT1 citrate (si)-synthase, mitochondrial YNR017W MAS6 MITOCHONDRIAL INNER MEMBRANE IMPORT TRANSLOCASE SUBUNIT mitochondrial inner membrane [O] MAS6 mitochondrial inner membrane import translocase subunit YOL023W IFM1 TRANSLATION INITIATION FACTOR 2,MITOCHONDRIAL mitochondria [P] IFM1 translation initiation factor 2, mitochondrial YOL077W-A ATP19 SUBUNIT K OF THE DIMERIC FORM OF MITOCHONDRIAL F1F0-ATP SYNTHASE mitochondrial inner membrane [E] ATP19 subunit K of the dimeric form of mitochondrial F1F0-ATP synthase YOR020C HSP10 CHAPERONIN,MITOCHONDRIAL mitochondrial matrix [F] HSP10 chaperonin, mitochondrial YOR065W CYT1 CYTOCHROME-C1 mitochondrial inner membrane [E] CYT1 cytochrome-c1 YOR136W IDH2 ISOCITRATE DEHYDROGENASE (NAD+) SUBUNIT 2,MITOCHONDRIAL mitochondrial matrix [E] IDH2 isocitrate dehydrogenase (NAD+) subunit 2, mitochondrial YOR142W LSC1 SUCCINATE-COA LIGASE ALPHA SUBUNIT mitochondrial matrix [E] LSC1 succinate-CoA ligase alpha subunit YOR158W PET123 RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] PET123 ribosomal protein, mitochondrial YOR176W HEM15 FERROCHELATASE PRECURSOR mitochondrial inner membrane [M] HEM15 ferrochelatase precursor YOR187W TUF1 TRANSLATION ELONGATION FACTOR TU,MITOCHONDRIAL mitochondrial matrix [P] TUF1 translation elongation factor TU, mitochondrial YOR222W ODC2 SIMILARITY TO ADP/ATP CARRIER PROTEINS mitochondrial inner membrane [O] ODC2 similarity to ADP/ATP carrier proteins YOR334W MRS2 RNA SPLICING PROTEIN AND MEMBER OF THE MITOCHONDRIAL CARRIER FAMILY (MCF) mitochondrial inner membrane [T] MRS2 RNA splicing protein and member of the mitochondrial carrier family (MCF) YOR374W ALD4 ALDEHYDE DEHYDROGENASE,MITOCHONDRIAL mitochondrial matrix [U] ALD4 aldehyde dehydrogenase, mitochondrial YPL029W SUV3 ATP-DEPENDENT RNA HELICASE,MITOCHONDRIAL mitochondrial matrix [T] SUV3 ATP-dependent RNA helicase, mitochondrial YPL078C ATP4 F1F0-ATPASE COMPLEX,F0 SUBUNIT B mitochondrial inner membrane [E] ATP4 F1F0-ATPase complex, F0 subunit B YPL134C ODC1 SIMILARITY TO ADP,ATP CARRIER PROTEINS mitochondrial inner membrane [A] ODC1 similarity to ADP,ATP carrier proteins YPL173W MRPL40 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT (YML40),MITOCHONDRIAL mitochondrial matrix [P] MRPL40 ribosomal protein of the large subunit (YmL40), mitochondrial YPL215W CBP3 REQUIRED FOR ASSEMBLY OF CYTOCHROME BC1 COMPLEX mitochondria [F] CBP3 required for assembly of cytochrome bc1 complex YPL262W FUM1 FUMARATE HYDRATASE mitochondrial matrix [E] FUM1 fumarate hydratase YPL270W MDL2 ATP-BINDING CASSETTE (ABC) TRANSPORTER FAMILY MEMBER mitochondrial inner membrane [A] MDL2 ATP-binding cassette (ABC) transporter family member YPR020W ATP20 SUBUNIT G OF THE DIMERIC FORM OF MITOCHONDRIAL F1F0-ATP SYNTHASE mitochondrial inner membrane [E] ATP20 subunit G of the dimeric form of mitochondrial F1F0-ATP Synthase YPR024W YME1 PROTEASE OF THE SEC18/CDC48/PAS1 FAMILY OF ATPASES (AAA) mitochondrial inner membrane [F] YME1 protease of the SEC18/CDC48/PAS1 family of ATPases (AAA) YPR047W MSF1 PHENYLALANINE--TRNA LIGASE ALPHA CHAIN,MITOCHONDRIAL mitochondrial matrix [P] MSF1 phenylalanine--tRNA ligase alpha chain, mitochondrial YPR133W-A TOM5 MITOCHONDRIAL OUTER MEMBRANE PROTEIN mitochondrial outer membrane [O] TOM5 mitochondrial outer membrane protein YPR191W QCR2 UBIQUINOL--CYTOCHROME-C REDUCTASE 40KD CHAIN II mitochondrial inner membrane [E] QCR2 ubiquinol--cytochrome-c reductase 40KD chain II YBL015W ACH1 mitochondrial matrix [M] ACH1 acetyl-CoA hydrolase YBL030C PET9 mitochondrial inner membrane [E] PET9 ADP/ATP carrier protein (MCF) YCL017C NFS1 mitochondrial matrix [A] NFS1 regulates Iron-Sulfur cluster proteins, cellular Iron uptake, andIron distribution YDR116C mitochondrial matrix [P] YDR116c similarity to bacterial ribosomal L1 proteins YDR234W LYS4 mitochondria [G] LYS4 homoaconitase YDR494W mitochondria [U] RCT1 weak similarity to hypothetical protein D. melanogaster YIL094C LYS12 mitochondria [G] LYS12 homo-isocitrate dehydrogenase YJL045W mitochondria [M] YJL045w strong similarity to succinate dehydrogenase flavoprotein YKR042W UTH1 mitochondrial outer membrane [C] UTH1 involved in the aging process YLR304C ACO1 mitochondrial matrix [E] ACO1 aconitate hydratase YML086C ALO1 mitochondria [M] ALO1 D-arabinono-1,4-lactone oxidase YMR158W mitochondrial matrix [U] YMR158w weak similarity to E.coli ribosomal S8 protein YMR241W YHM2 mitochondrial inner membrane [D] YHM2 yeast suppressor gene of HM (mitochondrial histone) mutant (ABF2) YNL055C POR1 mitochondrial outer membrane [O] POR1 mitochondrial outer membrane porin YNL104C LEU4 mitochondrial matrix [G] LEU4 2-isopropylmalalate synthase YPL013C mitochondrial matrix [P] YPL013c strong similarity to N.crassa mitochondrial ribosomal protein S24 YPL059W GRX5 mitochondrial matrix [R] GRX5 member of the subfamily of yeast glutaredoxins (Grx3, GRX4, and Grx5) YPL063W mitochondrial inner membrane [U] YPL063w similarity to hypothetical protein YLR019w, YLL010c and S.pombe hypothetical protein SPAC2F7.02c Q0050 AI1 COX1 INTRON 1 PROTEIN mitochondria [U] AI1 COX1 intron 1 protein YAL044C GCV3 GLYCINE DECARBOXYLASE,SUBUNIT H mitochondrial matrix [G] GCV3 glycine decarboxylase, subunit H YBL022C PIM1 ATP-DEPENDENT PROTEASE,MITOCHONDRIAL mitochondrial matrix [F] PIM1 ATP-dependent protease, mitochondrial YBR003W COQ1 HEXAPRENYL PYROPHOSPHATE SYNTHETASE PRECURSOR mitochondria [M] COQ1 hexaprenyl pyrophosphate synthetase precursor YBR044C TCM62 CHAPERONE REQUIRED FOR ASSEMBLY OF MITOCHONDRIAL SUCCINATE DEHYDROGENASE mitochondrial inner membrane [F] TCM62 chaperone required for assembly of mitochondrial succinate dehydrogenase YBR146W MRPS9 RIBOSOMAL PROTEIN S9 PRECURSOR,MITOCHONDRIAL mitochondrial matrix [P] MRPS9 ribosomal protein S9 precursor, mitochondrial YBR179C FZO1 REQUIRED FOR BIOGENESIS OF MITOCHONDRIA mitochondrial outer membrane [C] FZO1 required for biogenesis of mitochondria YBR251W MRPS5 RIBOSOMAL PROTEIN S5,MITOCHONDRIAL mitochondrial matrix [P] MRPS5 ribosomal protein S5, mitochondrial YDL120W YFH1 REGULATES MITOCHONDRIAL IRON ACCUMULATION mitochondrial matrix [A] YFH1 regulates mitochondrial iron accumulation YDL178W AIP2 ACTIN INTERACTING PROTEIN 2 mitochondrial matrix - - YDL181W INH1 INHIBITOR OF MITOCHONDRIAL ATPASE mitochondrial inner membrane [E] INH1 inhibitor of mitochondrial ATPase YDL202W MRPL11 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL11 ribosomal protein of the large subunit, mitochondrial YDR175C RSM24 COMPONENT OF THE MITOCHONDRIAL RIBOSOMAL SMALL SUBUNIT mitochondrial matrix [P] RSM24 component of the mitochondrial ribosomal small subunit YDR194C MSS116 RNA HELICASE OF THE DEAD BOX FAMILY,MITOCHONDRIAL mitochondrial matrix [T] MSS116 RNA helicase of the DEAD box family, mitochondrial YDR204W COQ4 RESPONSIBLE FOR RESTORING UBIQUINONE BIOSYNTHESIS IN COQ4 MUTANT mitochondrial inner membrane [M] COQ4 responsible for restoring ubiquinone biosynthesis in COQ4 mutant YDR237W MRPL7 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL7 ribosomal protein of the large subunit, mitochondrial YDR268W MSW1 TRYPTOPHANYL-TRNA SYNTHETASE,MITOCHONDRIAL mitochondrial matrix [P] MSW1 tryptophanyl-tRNA synthetase, mitochondrial YDR322C-A TIM11 SUBUNIT E OF THE DIMERIC FORM OF MITOCHONDRIAL F1F0-ATPASE mitochondrial inner membrane [E] TIM11 subunit E of the dimeric form of mitochondrial F1F0-ATPase YDR322W MRPL35 RIBOSOMAL PROTEIN YML35 OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL35 ribosomal protein YmL35 of the large subunit, mitochondrial YDR347W MRP1 RIBOSOMAL PROTEIN OF THE SMALL SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRP1 ribosomal protein of the small subunit, mitochondrial YEL050C RML2 RIBOSOMAL L2 PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] RML2 ribosomal L2 protein, mitochondrial YER069W ARG5,6 ACETYLGLUTAMATE KINASE AND ACETYLGLUTAMYL-PHOSPHATE REDUCTASE mitochondrial matrix [G] ARG5,6 acetylglutamate kinase and acetylglutamyl-phosphate reductase YER178W PDA1 PYRUVATE DEHYDROGENASE (LIPOAMIDE) ALPHA CHAIN PRECURSOR mitochondrial matrix [E] PDA1 pyruvate dehydrogenase (lipoamide) alpha chain precursor YFL036W RPO41 DNA-DIRECTED RNA POLYMERASE,MITOCHONDRIAL mitochondrial matrix [T] RPO41 DNA-directed RNA polymerase, mitochondrial YGL143C MRF1 PEPTIDE CHAIN RELEASE FACTOR,MITOCHONDRIAL mitochondrial matrix [P] MRF1 peptide chain release factor, mitochondrial YGR084C MRP13 RIBOSOMAL PROTEIN OF THE SMALL SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRP13 ribosomal protein of the small subunit, mitochondrial YGR193C PDX1 PYRUVATE DEHYDROGENASE COMPLEX PROTEIN X mitochondrial matrix [E] PDX1 pyruvate dehydrogenase complex protein X YHL004W MRP4 RIBOSOMAL PROTEIN OF THE SMALL SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRP4 ribosomal protein of the small subunit, mitochondrial YHR005C-A MRS11 SUBUNIT OF THE TIM22-COMPLEX mitochondrial intermembrane space [O] MRS11 subunit of the TIM22-complex YHR037W PUT2 1-PYRROLINE-5-CARBOXYLATE DEHYDROGENASE mitochondrial matrix [G] PUT2 1-pyrroline-5-carboxylate dehydrogenase YHR106W TRR2 THIOREDOXIN REDUCTASE mitochondria [M] TRR2 thioredoxin reductase YIL070C MAM33 MITOCHONDRIAL ACIDIC MATRIX PROTEIN mitochondrial matrix - - YJL112W MDV1 SIMILARITY TO MET30P AND N.CRASSA SULFUR CONTROLLER-2 mitochondrial outer membrane [U] MDV1 similarity to MET30P and N.crassa sulfur controller-2 YJR048W CYC1 CYTOCHROME-C ISOFORM 1 mitochondrial intermembrane space [E] CYC1 cytochrome-c isoform 1 YJR144W MGM101 MITOCHONDRIAL GENOME MAINTENANCE PROTEIN mitochondrial matrix [D] MGM101 mitochondrial genome maintenance protein YKL003C MRP17 RIBOSOMAL PROTEIN OF THE SMALL SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRP17 ribosomal protein of the small subunit, mitochondrial YKL011C CCE1 CRUCIFORM-CUTTING ENDONUCLEASE,MITOCHONDRIAL mitochondrial inner membrane [D] CCE1 cruciform-cutting endonuclease, mitochondrial YKL192C ACP1 MITOCHONRIAL ACYL-CARRIER PROTEIN mitochondrial matrix [M] ACP1 mitochonrial acyl-carrier protein YKR006C MRPL13 RIBOSOMAL PROTEIN YML13,MITOCHONDRIAL mitochondrial matrix [P] MRPL13 ribosomal protein YmL13, mitochondrial YKR052C MRS4 RNA SPLICING PROTEIN AND MEMBER OF THE MITOCHONDRIAL CARRIER FAMILY (MCF) mitochondrial inner membrane [O] MRS4 RNA splicing protein and member of the mitochondrial carrier family (MCF) YKR085C MRPL20 RIBOSOMAL PROTEIN YML20,MITOCHONDRIAL mitochondrial matrix [P] MRPL20 ribosomal protein YmL20, mitochondrial YLR038C COX12 CYTOCHROME-C OXIDASE,SUBUNIT VIB mitochondrial inner membrane [E] COX12 cytochrome-c oxidase, subunit VIB YLR295C ATP14 F1F0-ATPASE COMPLEX,SUBUNIT H mitochondrial inner membrane [E] ATP14 F1F0-ATPase complex, subunit h YLR312W-A MRPL15 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL15 ribosomal protein of the large subunit, mitochondrial YLR382C NAM2 LEUCINE--TRNA LIGASE PRECURSOR,MITOCHONDRIAL mitochondrial matrix [P] NAM2 leucine--tRNA ligase precursor, mitochondrial YML078W CPR3 CYCLOPHILIN (PEPTIDYLPROLYL ISOMERASE),MITOCHONDRIAL mitochondrial matrix [F] CPR3 cyclophilin (peptidylprolyl isomerase), mitochondrial YML110C COQ5 UBIQUINONE BIOSYNTHESIS,METHYLTRANSFERASE mitochondria [M] COQ5 ubiquinone biosynthesis, methyltransferase YMR024W MRPL3 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL3 ribosomal protein of the large subunit, mitochondrial YMR189W GCV2 GLYCINE DECARBOXYLASE P SUBUNIT mitochondrial matrix [G] GCV2 glycine decarboxylase P subunit YNL306W RIBOSOMAL PROTEIN OF THE SMALL SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPS18 ribosomal protein of the small subunit, mitochondrial YOL140W ARG8 ACETYLORNITHINE AMINOTRANSFERASE mitochondrial matrix [G] ARG8 acetylornithine aminotransferase YOR201C PET56 RRNA (GUANOSINE-2'-O-)-METHYLTRANSFERASE mitochondria [T] PET56 rRNA (guanosine-2'-O-)-methyltransferase YOR232W MGE1 HEAT SHOCK PROTEIN - CHAPERONE mitochondrial matrix [F] MGE1 heat shock protein - chaperone YPL097W MSY1 TYROSYL-TRNA SYNTHETASE mitochondrial matrix [P] MSY1 tyrosyl-tRNA synthetase YPL271W ATP15 F1F0-ATPASE COMPLEX,F1 EPSILON SUBUNIT mitochondrial inner membrane [E] ATP15 F1F0-ATPase complex, F1 epsilon subunit YPR067W ISA2 MITOCHONDRIAL PROTEIN REQUIRED FOR IRON METABOLISM mitochondrial intermembrane space [A] ISA2 mitochondrial protein required for iron metabolism YBR026C (MRF1) mitochondria [B] (MRF1) mitochondrial respiratory function protein YCR028C-A RIM1 SSDNA-BINDING PROTEIN,MITOCHONDRIAL mitochondrial matrix [D] RIM1 ssDNA-binding protein, mitochondrial YDR511W ACN9 mitochondrial intermembrane space [U] ACN9 weak similarity to C. elegans protein F25H9.7 and to the human complement 3 precursor YGL129C RSM23 mitochondrial matrix [U] RSM23 similarity to S.pombe hypothetical protein SPBC29A3.15C - putative mitochondrial function YGR094W VAS1 mitochondrial matrix [P] VAS1 valyl-tRNA synthetase YGR165W mitochondrial matrix [U] YGR165w similarity to PIR:T39444 hypothetical protein SPBC14C8.16c S. pombe YJR104C SOD1 mitochondrial intermembrane space [R] SOD1 copper-zinc superoxide dismutase YNL177C mitochondrial matrix [U] YNL177c similarity to hypothetical protein S. pombe YOR221C MCT1 mitochondria [M] MCT1 malonyl-CoA:ACP transferase YPR100W mitochondrial matrix [U] YPR100w weak similarity to C.elegans hypothetical protein CEC25A1 Q0140 VAR1 MITOCHONDRIAL RIBOSOMAL PROTEIN mitochondrial matrix [P] VAR1 mitochondrial ribosomal protein YAR035W YAT1 CARNITINE ACETYLTRANSFERASE,MITOCHONDRIAL mitochondrial outer membrane [M] YAT1 carnitine acetyltransferase, mitochondrial YBL038W MRPL16 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL16 ribosomal protein of the large subunit, mitochondrial YBL090W MRP21 MITOCHONDRIAL RIBOSOMAL PROTEIN mitochondrial matrix [P] MRP21 Mitochondrial ribosomal protein YBR120C CBP6 APO-CYTOCHROME B PRE-MRNA PROCESSING PROTEIN mitochondria [P] CBP6 apo-cytochrome B pre-mRNA processing protein YBR291C CTP1 CITRATE TRANSPORT PROTEIN,MITOCHONDRIAL (MCF) mitochondrial inner membrane [O] CTP1 citrate transport protein, mitochondrial (MCF) YCL057W PRD1 PROTEINASE YSCD mitochondrial intermembrane space [F] PRD1 proteinase yscD YDL067C COX9 CYTOCHROME-C OXIDASE CHAIN VIIA mitochondrial inner membrane [E] COX9 cytochrome-c oxidase chain VIIA YDR462W MRPL28 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT (YML28),MITOCHONDRIAL mitochondrial matrix [P] MRPL28 ribosomal protein of the large subunit (YmL28), mitochondrial YER050C RSM18 COMPONENT OF THE MITOCHONDRIAL RIBOSOMAL SMALL SUBUNIT mitochondrial matrix [P] RSM18 component of the mitochondrial ribosomal small subunit YER061C CEM1 BETA-KETO-ACYL-ACP SYNTHASE,MITOCHONDRIAL mitochondria [E] CEM1 beta-keto-acyl-ACP synthase, mitochondrial YFR049W YMR31 RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] YMR31 ribosomal protein, mitochondrial YGR144W THI4 INVOLVED IN THIAMINE BIOSYNTHESIS AND DNA REPAIR mitochondria [D] THI4 involved in thiamine biosynthesis and DNA repair YGR220C MRPL9 RIBOSOMAL PROTEIN YML9,MITOCHONDRIAL mitochondrial matrix [P] MRPL9 ribosomal protein YmL9, mitochondrial YHR001W-A QCR10 UBIQUINOL--CYTOCHROME-C REDUCTASE 8.5 KDA SUBUNIT mitochondrial inner membrane [E] QCR10 ubiquinol--cytochrome-c reductase 8.5 kDa subunit YIL134W FLX1 FAD CARRIER PROTEIN (MCF),MITOCHONDRIAL mitochondrial inner membrane [O] FLX1 FAD carrier protein (MCF), mitochondrial YKL170W MRPL38 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT (L14),MITOCHONDRIAL mitochondrial matrix [P] MRPL38 ribosomal protein of the large subunit (L14), mitochondrial YKL194C MST1 THREONINE--TRNA LIGASE,MITOCHONDRIAL mitochondrial matrix [P] MST1 threonine--tRNA ligase, mitochondrial YLR142W PUT1 PROLINE OXIDASE mitochondria [G] PUT1 proline oxidase YLR348C DIC1 DICARBOXYLATE CARRIER PROTEIN mitochondrial inner membrane [O] DIC1 dicarboxylate carrier protein YLR393W ATP10 F1F0 ATPASE COMPLEX ASSEMBLY PROTEIN mitochondrial inner membrane [F] ATP10 F1F0 ATPase complex assembly protein YLR439W MRPL4 RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] MRPL4 ribosomal protein, mitochondrial YMR193W MRPL24 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL24 ribosomal protein of the large subunit, mitochondrial YMR302C PRP12 INVOLVED IN EARLY MATURATION OF PRE-RRNA mitochondrial inner membrane [T] PRP12 involved in early maturation of pre-rRNA YNL125C ESBP6 SIMILARITY TO YKL221W AND HUMAN X-LINKED PEST-CONTAINING TRANSPORTER mitochondrial inner membrane [A] ESBP6 similarity to YKL221w and human X-linked PEST-containing transporter YNL137C NAM9 RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] NAM9 ribosomal protein, mitochondrial YOR150W MRPL23 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT,MITOCHONDRIAL mitochondrial matrix [P] MRPL23 ribosomal protein of the large subunit, mitochondrial YOR330C MIP1 DNA-DIRECTED DNA POLYMERASE GAMMA CATALYTIC SUBUNIT,MITOCHONDRIAL mitochondrial matrix [D] MIP1 DNA-directed DNA polymerase gamma catalytic subunit, mitochondrial YOR356W STRONG SIMILARITY TO HUMAN ELECTRON TRANSFER FLAVOPROTEIN-UBIQUINONE OXIDOREDUCTASE mitochondria [E] YOR356w strong similarity to human electron transfer flavoprotein-ubiquinone oxidoreductase YPL040C ISM1 ISOLEUCINE--TRNA LIGASE,MITOCHONDRIAL mitochondria [P] ISM1 isoleucine--tRNA ligase, mitochondrial YPL118W MRP51 MITOCHONDRIAL RIBOSOMAL PROTEIN OF THE SMALL SUBUNIT mitochondrial matrix [P] MRP51 mitochondrial ribosomal protein of the small subunit YPR006C ICL2 NON-FUNCTIONAL ISOCITRATE LYASE mitochondrial matrix [M] ICL2 non-functional isocitrate lyase YPR058W YMC1 MITOCHONDRIAL CARRIER PROTEIN (MCF) mitochondrial inner membrane [O] YMC1 mitochondrial carrier protein (MCF) Q0110 BI2 MRNA MATURASE BI2 mitochondria [T] BI2 mRNA maturase BI2 Q0115 BI3 MRNA MATURASE BI3 mitochondria [T] BI3 mRNA maturase BI3 YDR263C DIN7 DNA-DAMAGE INDUCIBLE PROTEIN mitochondrial matrix [R] DIN7 DNA-damage inducible protein YGL018C JAC1 MOLECULAR CHAPERONE mitochondrial matrix [F] JAC1 molecular chaperone YGL023C PIB2 PHOSPHATIDYLINOSITOL 3-PHOSPHATE BINDING mitochondria [U] PIB2 phosphatidylinositol 3-phosphate binding YGL125W MET13 PUTATIVE METHYLENE TETRAHYDROFOLATE REDUCTASE mitochondria [G] MET13 putative methylene tetrahydrofolate reductase YGR112W SHY1 SURF HOMOLOGUE PROTEIN mitochondrial inner membrane [E] SHY1 SURF homologue protein YKL167C MRP49 RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] MRP49 ribosomal protein, mitochondrial YDL044C MTF2 MITOCHONDRIAL PROTEIN INVOLVED IN MRNA SPLICING AND PROTEIN SYNTHESIS mitochondrial matrix [P] MTF2 mitochondrial protein involved in mRNA splicing and protein synthesis YGR174C CBP4 UBIQUINOL--CYTOCHROME-C REDUCTASE ASSEMBLY FACTOR mitochondria [F] CBP4 ubiquinol--cytochrome-c reductase assembly factor YJR095W SFC1 SUCCINATE-FUMARATE TRANSPORTER mitochondrial inner membrane [A] SFC1 succinate-fumarate transporter YPR001W CIT3 CITRATE (SI)-SYNTHASE,MITOCHONDRIAL mitochondrial matrix [E] CIT3 citrate (si)-synthase, mitochondrial YBR104W YMC2 MITOCHONDRIAL CARRIER PROTEIN (MCF) mitochondrial inner membrane [O] YMC2 mitochondrial carrier protein (MCF) YCR046C IMG1 RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] IMG1 ribosomal protein, mitochondrial YDL085W MITOCHONDRIAL NADH DEHYDROGENASE THAT CATALYZES THE OXIDATION OF CYTOSOLIC NADH mitochondrial inner membrane [E] NDH2 mitochondrial NADH dehydrogenase that catalyzes the oxidation of cytosolic NADH YDL130W-A STF1 ATPASE STABILIZING FACTOR,10 KDA mitochondrial inner membrane [E] STF1 ATPase stabilizing factor, 10 kDa YDR041W RSM10 COMPONENT OF THE MITOCHONDRIAL RIBOSOMAL SMALL SUBUNIT mitochondrial matrix [P] RSM10 component of the mitochondrial ribosomal small subunit YEL020W-A TIM9 ESSENTIAL SUBUNIT OF THE TIM22-COMPLEX FOR MITOCHONDRIAL PROTEIN IMPORT mitochondrial intermembrane space [O] TIM9 essential subunit of the TIM22-complex for mitochondrial protein import YFR033C QCR6 UBIQUINOL--CYTOCHROME-C REDUCTASE 17K PROTEIN mitochondrial inner membrane [E] QCR6 ubiquinol--cytochrome-c reductase 17K protein YGR181W TIM13 TRANSLOCASE OF THE INNER MEMBRANE mitochondrial intermembrane space [F] TIM13 Translocase of the inner membrane YIL098C FMC1 FORMATION OF MITOCHONDRIAL CYTOCHROMES mitochondrial matrix [M] FMC1 Formation of Mitochondrial Cytochromes YJL066C MPM1 HYPOTHETICAL PROTEIN mitochondria [U] MPM1 hypothetical protein YJL071W ARG2 ACETYLGLUTAMATE SYNTHASE mitochondrial matrix [G] ARG2 acetylglutamate synthase YKL106W AAT1 ASPARTATE TRANSAMINASE,MITOCHONDRIAL mitochondria [G] AAT1 aspartate transaminase, mitochondrial YKL208W CBT1 APO-CYTOCHROME B PRE-MRNA PROCESSING PROTEIN mitochondria [T] CBT1 apo-cytochrome b pre-mRNA processing protein YLL001W DNM1 DYNAMIN-RELATED PROTEIN mitochondrial outer membrane - - YLL006W MMM1 REQUIRED FOR MITOCHONDRIAL SHAPE AND STRUCTURE mitochondrial outer membrane - - YLR203C MSS51 POSSIBLY INVOLVED IN TRANSLATIONAL ACTIVATION OF COX1 AND COB MRNA mitochondrial inner membrane [P] MSS51 possibly involved in translational activation of COX1 and COB mRNA YLR369W SSQ1 MITOCHONDRIAL HEAT SHOCK PROTEIN 70 mitochondrial matrix [F] SSQ1 mitochondrial heat shock protein 70 YMR177W MMT1 MITOCHONDRIAL GENE INVOLVED IN IRON UPTAKE mitochondrial inner membrane [A] MMT1 mitochondrial gene involved in iron uptake YMR267W PPA2 INORGANIC PYROPHOSPHATASE,MITOCHONDRIAL mitochondria [E] PPA2 inorganic pyrophosphatase, mitochondrial YMR293C SIMILARITY TO AMIDASES mitochondria [M] YMR293c similarity to amidases YNL252C MRPL17 RIBOSOMAL PROTEIN OF THE LARGE SUBUNIT (YML30),MITOCHONDRIAL mitochondrial matrix [P] MRPL17 ribosomal protein of the large subunit (YmL30), mitochondrial YOR211C MGM1 DYNAMIN-LIKE PROTEIN mitochondrial inner membrane - - YPL104W MSD1 ASPARTATE--TRNA LIGASE,MITOCHONDRIAL mitochondria [P] MSD1 aspartate--tRNA ligase, mitochondrial YDR513W TTR1 mitochondria [R] TTR1 glutaredoxin YML042W CAT2 mitochondrial matrix [M] CAT2 carnitine O-acetyltransferase YML061C PIF1 mitochondrial matrix [D] PIF1 DNA helicase involved in mitochondrial DNA repair and telomere length YNR037C RSM19 mitochondrial matrix [P] RSM19 strong similarity to Mycoplasma ribosomal protein S19 Q0120 BI4 MRNA MATURASE BI4 mitochondria [T] BI4 mRNA maturase BI4 YDR231C COX20 IN THE MATURATION AND ASSEMBLY OF CYTOCHROME OXIDASE INVOLVED PROTEIN mitochondrial inner membrane [E] COX20 in the maturation and assembly of cytochrome oxidase involved protein YIL065C FIS1 PROTEIN INVOLVED IN MITOCHONDRIAL DIVISION mitochondrial outer membrane [C] FIS1 protein involved in mitochondrial division YPL224C MMT2 MITOCHONDRIAL IRON TRANSPORTER mitochondrial inner membrane [O] MMT2 mitochondrial iron transporter YER053C mitochondrial inner membrane [O] YER053c strong similarity to mitochondrial phosphate carrier protein YJL003W mitochondrial inner membrane [U] YJL003w weak similarity to hypothetical protein SPAC1486.08 S. pombe Q0075 AI5_BETA COX1 INTRON PROTEIN AI5-BETA mitochondria - - YCR083W TRX3 MITOCHONDRIAL THIOREDOXIN mitochondria [R] TRX3 mitochondrial thioredoxin YGL119W ABC1 UBIQUINOL--CYTOCHROME-C REDUCTASE COMPLEX ASSEMBLY PROTEIN mitochondria [F] ABC1 ubiquinol--cytochrome-c reductase complex assembly protein YGR029W ERV1 MITOCHONDRIAL BIOGENESIS AND REGULATION OF CELL CYCLE mitochondrial intermembrane space [D] ERV1 mitochondrial biogenesis and regulation of cell cycle YHR076W WEAK SIMILARITY TO C.ELEGANS HYPOTHETICAL PROTEIN CEW09D10 mitochondria [E] YHR076w weak similarity to C.elegans hypothetical protein CEW09D10 YHR091C MSR1 ARGINYL-TRNA SYNTHETASE,MITOCHONDRIAL mitochondrial matrix [P] MSR1 arginyl-tRNA synthetase, mitochondrial YJR101W RSM26 WEAK SIMILARITY TO SUPEROXIDE DISMUTASES mitochondrial matrix [U] RSM26 weak similarity to superoxide dismutases YJR135W-A TIM8 DELIVERS PROTEINS ACROSS THE INTERMEMBRANE SPACE OF MITOCHONDRIA TO THE TIM22 COMPLEX mitochondrial intermembrane space [O] TIM8 delivers Proteins across the intermembrane space of mitochondria to the TIM22 complex YLR139C SLS1 SUPPRESSES LETHALITY OF SSM4 DELETION mitochondrial inner membrane [T] SLS1 suppresses lethality of SSM4 deletion YMR023C MSS1 MITOCHONDRIAL GTPASE INVOLVED IN EXPRESSION OF COX1 mitochondrial inner membrane [T] MSS1 mitochondrial GTPase involved in expression of COX1 YMR257C PET111 REQUIRED FOR TRANSLATION OF COX2 MRNA mitochondrial inner membrane [P] PET111 required for translation of COX2 mRNA YNR041C COQ2 PARA-HYDROXYBENZOATE--POLYPRENYLTRANSFERASE mitochondrial inner membrane [M] COQ2 para-hydroxybenzoate--polyprenyltransferase YCR071C IMG2 mitochondrial matrix [C] IMG2 required for Integrity of Mitochondrial Genome YLR239C LIP2 mitochondrial matrix [M] LIP2 lipoic acid ligase YML025C RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] YML6 ribosomal protein, mitochondrial YNR022C mitochondrial matrix [U] YNR022c weak similarity to protein phosphatases YER168C CCA1 mitochondrial matrix [T] CCA1 tRNA nucleotidyltransferase YBR185C MBA1 RESPIRATORY CHAIN ASSEMBLY PROTEIN mitochondrial inner membrane [F] MBA1 respiratory chain assembly protein YDL069C CBS1 TRANSLATIONAL ACTIVATOR OF COB MRNA mitochondrial inner membrane [P] CBS1 translational activator of COB mRNA YDR296W MHR1 mitochondrial matrix [D] MHR1 Involved in mitochondrial homologous DNA recombination YDR393W SHE9 mitochondrial inner membrane [U] SHE9 weak similarity to rabbit trichohyalin YGR183C QCR9 UBIQUINOL--CYTOCHROME-C REDUCTASE SUBUNIT 9 mitochondrial inner membrane [E] QCR9 ubiquinol--cytochrome-c reductase subunit 9 YJL023C PET130 PROTEIN SYNTHESIS PROTEIN,MITOCHONDRIAL mitochondria [P] PET130 protein synthesis protein, mitochondrial YJL054W TIM54 TRANSLOCASE FOR THE INSERTION OF PROTEINS INTO THE MITOCHONDRIAL INNER MEMBRANE mitochondrial inner membrane [O] TIM54 translocase for the insertion of proteins into the mitochondrial inner membrane YOR297C TIM18 COMPONENT OF THE INNER MITOCHONDRIAL MEMBRANE TRANSLOCATION COMPLEX mitochondrial inner membrane [F] TIM18 component of the inner mitochondrial membrane translocation complex YPL132W COX11 CYTOCHROME-C OXIDASE ASSEMBLY PROTEIN mitochondrial inner membrane [F] COX11 cytochrome-c oxidase assembly protein YPR033C HTS1 mitochondrial matrix [P] HTS1 histidine--tRNA ligase, mitochondrial YBL013W FMT1 METHIONYL-TRNA TRANSFORMYLASE mitochondrial matrix [T] FMT1 Methionyl-tRNA Transformylase YBR024W SCO2 INVOLVED IN STABILITY OF COX1P AND COX2P mitochondrial inner membrane [F] SCO2 involved in stability of COX1P and COX2P YCL004W PGS1 mitochondrial inner membrane [M] PGS1 phosphatidylglycerophosphate synthase YDR120C TRM1 mitochondrial matrix [T] TRM1 N2,N2-dimethylguanine tRNA methyltransferase YIL042C mitochondria [G] YIL042c similarity to rat branched-chain alpha-ketoacid dehydrogenase kinase YJL209W CBP1 APO-CYTOCHROME B PRE-MRNA PROCESSING PROTEIN mitochondria [T] CBP1 apo-cytochrome b pre-mRNA processing protein YKL087C CYT2 HOLOCYTOCHROME-C1 SYNTHASE mitochondrial intermembrane space [F] CYT2 holocytochrome-c1 synthase YML021C UNG1 mitochondria [D] UNG1 uracil-DNA glycosylase YNL073W MSK1 mitochondrial matrix [P] MSK1 lysyl-tRNA synthetase, mitochondrial YOR125C CAT5 INVOLVED IN COENZYME Q (UBIQUINONE) BIOSYNTHESIS mitochondrial inner membrane [M] CAT5 involved in coenzyme Q (ubiquinone) biosynthesis YDL107W MSS2 SER/THR PROTEIN KINASE mitochondrial inner membrane [E] MSS2 ser/thr protein kinase YPR011C mitochondrial inner membrane [O] YPR011c similarity to ADP/ATP carrier proteins and Graves disease carrier protein YDL164C CDC9 mitochondrial matrix [D] CDC9 DNA ligase YJR062C NTA1 mitochondria [F] NTA1 amino-terminal amidase YDR115W SIMILARITY TO BACTERIAL RIBOSOMAL L34 PROTEINS mitochondrial matrix [P] YDR115w similarity to bacterial ribosomal L34 proteins YEL006W mitochondrial inner membrane [A] YEL006w similarity to peroxisomal membrane and mitochondrial carrier proteins YLL027W ISA1 MITOCHONDRIAL PROTEIN REQUIRED FOR NORMAL IRON METABOLISM mitochondrial matrix [A] ISA1 mitochondrial protein required for normal iron metabolism YLR168C (MSF1) PROBABLY INVOLVED IN INTRAMITOCHONDRIAL PROTEIN SORTING mitochondria [F] (MSF1) probably involved in intramitochondrial protein sorting YNL169C PSD1 PHOSPHATIDYLSERINE DECARBOXYLASE 1 mitochondrial inner membrane [M] PSD1 phosphatidylserine decarboxylase 1 YOR045W TOM6 MITOCHONDRIAL OUTER MEMBRANE IMPORT RECEPTOR SUBUNIT,6 KD mitochondrial outer membrane [O] TOM6 mitochondrial outer membrane import receptor subunit, 6 kD Q0055 AI2 COX1 INTRON 2 PROTEIN mitochondria [U] AI2 COX1 intron 2 protein Q0060 AI3 DNA ENDONUCLEASE mitochondria [U] AI3 DNA endonuclease Q0065 AI4 DNA ENDONUCLEASE mitochondria [U] AI4 DNA endonuclease Q0160 SCEI DNA ENDONUCLEASE IN 21S RRNA INTRON mitochondria [T] SCEI DNA endonuclease in 21S rRNA intron YOR037W CYC2 CYTOCHROME-C MITOCHONDRIAL IMPORT FACTOR mitochondrial inner membrane [O] CYC2 cytochrome-c mitochondrial import factor YGR171C MSM1 METHIONYL-TRNA SYNTHETASE mitochondrial matrix [P] MSM1 methionyl-tRNA synthetase YHL038C CBP2 APO-CYTOCHROME B PRE-MRNA PROCESSING PROTEIN 2 mitochondria [T] CBP2 apo-cytochrome b pre-mRNA processing protein 2 YMR152W YIM1 MITOCHONDRIAL INNER MEMBRANE PROTEASE mitochondrial inner membrane [F] YIM1 mitochondrial inner membrane protease YMR282C AEP2 REQUIRED FOR THE EXPRESSION OF SUBUNIT-9 OF ATP SYNTHASE mitochondria [P] AEP2 required for the expression of subunit-9 of atp synthase YOL033W MSE1 GLUTAMYL-TRNA SYNTHETASE,MITOCHONDRIAL mitochondrial matrix [P] MSE1 glutamyl-tRNA synthetase, mitochondrial YOR196C LIP5 LIPOIC ACID SYNTHASE mitochondrial matrix [M] LIP5 lipoic acid synthase YPR134W MSS18 SPLICING PROTEIN mitochondria [T] MSS18 splicing protein YER170W ADK2 ADENYLATE KINASE,MITOCHONDRIAL mitochondrial matrix [M] ADK2 adenylate kinase, mitochondrial YOL095C HMI1 MITOCHONDRIAL DNA HELICASE mitochondrial matrix [D] HMI1 mitochondrial DNA helicase YDR079W PET100 CYTOCHROME-C OXIDASE ASSEMBLY PROTEIN mitochondrial inner membrane [F] PET100 cytochrome-c oxidase assembly protein YOR017W PET127 COMPONENT OF MITOCHONDRIAL TRANSLATION SYSTEM mitochondrial inner membrane [P] PET127 component of mitochondrial translation system YJL063C MRPL8 RIBOSOMAL PROTEIN L17,MITOCHONDRIAL mitochondrial matrix [P] MRPL8 ribosomal protein L17, mitochondrial YKL138C MRPL31 RIBOSOMAL PROTEIN YML31,MITOCHONDRIAL mitochondrial matrix [P] MRPL31 ribosomal protein YmL31, mitochondrial YML009C MRPL39 60S RIBOSOMAL PROTEIN,MITOCHONDRIAL mitochondrial matrix [P] MRPL39 60S ribosomal protein, mitochondrial YPR166C MRP2 RIBOSOMAL PROTEIN S14 mitochondrial matrix [P] MRP2 ribosomal protein S14 YDL045W-A MRP10 MITOCHONDRIAL RIBOSOMAL PROTEIN mitochondrial matrix [P] MRP10 mitochondrial ribosomal protein YMR225C MRPL44 RIBOSOMAL PROTEIN YMR44,MITOCHONDRIAL mitochondrial matrix [P] MRPL44 ribosomal protein YMR44, mitochondrial YGR062C COX18 REQUIRED FOR ACTIVITY OF MITOCHONDRIAL CYTOCHROME OXIDASE mitochondrial inner membrane [E] COX18 required for activity of mitochondrial cytochrome oxidase YOL096C COQ3 ENZYME OF UBIQUINONE (COENZYME Q) BIOSYNTHESIS mitochondrial inner membrane [M] COQ3 enzyme of ubiquinone (coenzyme Q) biosynthesis YPL172C COX10 FARNESYL TRANSFERASE mitochondrial inner membrane [F] COX10 farnesyl transferase YDL142C CRD1 CARDIOLIPIN SYNTHASE mitochondrial inner membrane [M] CRD1 cardiolipin synthase YER153C PET122 TRANSLATIONAL ACTIVATOR OF CYTOCHROME C OXIDASE SUBUNIT III mitochondrial inner membrane [P] PET122 translational activator of cytochrome c oxidase subunit III YGR222W PET54 SPLICING PROTEIN AND TRANSLATIONAL ACTIVATOR,MITOCHONDRIAL mitochondrial matrix [P] PET54 splicing protein and translational activator, mitochondrial YLR067C PET309 REQUIRED FOR STABILITY AND TRANSLATION OF COX1 MRNA mitochondrial inner membrane [T] PET309 required for stability and translation of COX1 mRNA YMR035W IMP2 MITOCHONDRIAL INNER MEMBRANE PROTEASE SUBUNIT mitochondrial inner membrane [F] IMP2 mitochondrial inner membrane protease subunit YMR150C IMP1 PROTEASE,MITOCHONDRIAL mitochondrial inner membrane [F] IMP1 protease, mitochondrial YNR045W PET494 TRANSLATIONAL ACTIVATOR,MITOCHONDRIAL mitochondrial inner membrane [P] PET494 translational activator, mitochondrial YPL060W LPE10 STRONG SIMILARITY TO MRS2P mitochondrial inner membrane [T] LPE10 strong similarity to MRS2P Q0275 COX3 CYTOCHROME-C OXIDASE CHAIN III mitochondrial inner membrane [E] COX3 cytochrome-c oxidase chain III YDL217C TIM22 SUBUNIT OF THE TIM22-COMPLEX mitochondrial inner membrane [F] TIM22 subunit of the TIM22-complex YEL059C-A SOM1 REQUIRED FOR MITOCHONDRIAL IMP1 PEPTIDASE FUNCTION mitochondrial inner membrane [O] SOM1 required for mitochondrial IMP1 peptidase function YGR008C STF2 ATPASE STABILIZING FACTOR mitochondrial inner membrane [C] STF2 ATPase stabilizing factor YJL133W MRS3 RNA SPLICING PROTEIN AND MEMBER OF THE MITOCHONDRIAL CARRIER FAMILY (MCF) mitochondrial inner membrane [O] MRS3 RNA splicing protein and member of the mitochondrial carrier family (MCF) YJL143W TIM17 MITOCHONDRIAL INNER MEMBRANE IMPORT TRANSLOCASE SUBUNIT mitochondrial inner membrane [O] TIM17 mitochondrial inner membrane import translocase subunit YOR100C CRC1 MITOCHONDRIAL CARNITINE CARRIER,MEMBER OF THE MITOCHONDRIAL CARRIER (MCF) FAMILY mitochondrial inner membrane [O] CRC1 mitochondrial carnitine carrier, member of the mitochondrial carrier (MCF) family YOR130C ORT1 ORNITHINE TRANSPORT PROTEIN OF MITOCHONDRIA INVOLVED IN ARGININE METABOLISM,MEMBER OF THE MITOCHONDRIAL CARRIER FAMILY (MCF) mitochondrial inner membrane [O] ORT1 ornithine transport protein of mitochondria involved in arginine metabolism, member of the mitochondrial carrier family (MCF) YOR266W PNT1 PENTAMIDINE RESISTANCE FACTOR mitochondrial inner membrane [R] PNT1 pentamidine resistance factor Q0080 AAP1 F1F0-ATPASE COMPLEX,F0 SUBUNIT 8 mitochondrial inner membrane [E] AAP1 F1F0-ATPase complex, F0 subunit 8 Q0105 COB UBIQUINOL-CYTOCHROME-C REDUCTASE SUBUNIT (CYTOCHROME B) mitochondrial inner membrane [E] COB ubiquinol-cytochrome-c reductase subunit (cytochrome B) Q0130 OLI1 F1F0-ATPASE COMPLEX,F0 SUBUNIT 9 mitochondrial inner membrane [E] OLI1 F1F0-ATPase complex, F0 subunit 9 YFR045W SIMILARITY TO MITOCHONDRIAL CITRATE TRANSPORT PROTEINS mitochondrial inner membrane [A] YFR045w similarity to mitochondrial citrate transport proteins YER058W PET117 CYTOCHROME C OXIDASE ASSEMBLY FACTOR mitochondrial inner membrane [F] PET117 cytochrome c oxidase assembly factor YNL003C PET8 MEMBER OF THE MITOCHONDRIAL CARRIER (MCF) FAMILY mitochondrial inner membrane [O] PET8 member of the mitochondrial carrier (MCF) family YDR236C FMN1 RIBOFLAVIN KINASE mitochondrial inner membrane [U] FMN1 Riboflavin kinase YJR034W PET191 INVOLVED IN ASSEMBLY OF CYTOCHROME OXIDASE mitochondrial inner membrane [E] PET191 involved in assembly of cytochrome oxidase YBR091C MRS5 SUBUNIT OF THE TIM22-COMPLEX mitochondrial intermembrane space [F] MRS5 subunit of the TIM22-complex YDR226W ADK1 ADENYLATE KINASE,CYTOSOLIC mitochondrial intermembrane space [M] ADK1 adenylate kinase, cytosolic YLL009C COX17 INTERACTS GENETICALLY WITH SCO1 AND SCO2 IN CYTOCHROME OXIDASE ASSEMBLY mitochondrial intermembrane space [F] COX17 interacts genetically with SCO1 and SCO2 in cytochrome oxidase assembly YLR059C REX2 PUTATIVE 3'-5' EXONUCLEASE mitochondrial matrix [T] REX2 putative 3'-5' exonuclease YCR024C ASN-TRNA SYNTHETASE,MITOCHONDRIAL mitochondrial matrix [P] YCR024c asn-tRNA synthetase, mitochondrial YOR040W GLO4 GLYOXALASE II (HYDROXYACYLGLUTATHIONE HYDROLASE) mitochondrial matrix [M] GLO4 glyoxalase II (hydroxyacylglutathione hydrolase) YPL135W ISU1 STRONG SIMILARITY TO NITROGEN FIXATION PROTEIN (NIFU) mitochondrial matrix [M] ISU1 strong similarity to nitrogen fixation protein (nifU) YPL252C YAH1 SIMILARITY TO ADRENODOXIN AND FERRODOXIN mitochondrial matrix [U] YAH1 similarity to adrenodoxin and ferrodoxin YNL315C ATP11 F1F0-ATPASE COMPLEX ASSEMBLY PROTEIN mitochondrial matrix [F] ATP11 F1F0-ATPase complex assembly protein YOR226C ISU2 STRONG SIMILARITY TO NITROGEN FIXATION PROTEINS mitochondrial matrix [M] ISU2 strong similarity to nitrogen fixation proteins YBR268W MRPL37 RIBOSOMAL PROTEIN YML37,MITOCHONDRIAL mitochondrial matrix [P] MRPL37 ribosomal protein YmL37, mitochondrial YCR003W MRPL32 RIBOSOMAL PROTEIN YML32,MITOCHONDRIAL mitochondrial matrix [P] MRPL32 ribosomal protein YmL32, mitochondrial YAL010C MDM10 INVOLVED IN MITOCHONDRIAL MORPHOLOGY AND INHERITANCE mitochondrial outer membrane - - YOL009C MDM12 INVOLVED IN MITOCHONDRIAL INHERITANCE mitochondrial outer membrane - - YDR470C UGO1 SIMILARITY TO CHROMOSOME SEGREGATION PROTEIN CSE1P mitochondrial outer membrane [U] UGO1 similarity to chromosome segregation protein CSE1P YGR028W MSP1 INTRA-MITOCHONDRIAL SORTING PROTEIN mitochondrial outer membrane [O] MSP1 intra-mitochondrial sorting protein YIL114C POR2 VOLTAGE DEPENDENT ANION CHANNEL (YVDAC2) mitochondrial outer membrane [A] POR2 voltage dependent anion channel (YVDAC2) YMR060C TOM37 MITOCHONDRIAL OUTER MEMBRANE IMPORT RECEPTOR SUBUNIT,37 KD mitochondrial outer membrane [O] TOM37 mitochondrial outer membrane import receptor subunit, 37 kD YAL015C NTG1 mitochondria [D] NTG1 DNA repair protein YAL033W POP5 mitochondrial matrix [T] POP5 required for processing of tRNAs and rRNAs YBL018C POP8 mitochondrial matrix [T] POP8 required for processing of tRNAs and rRNAs YBR029C CDS1 mitochondria [M] CDS1 CDP-diacylglycerol synthase YBR121C GRS1 mitochondria [P] GRS1 glycine--tRNA ligase YBR167C POP7 mitochondrial matrix [T] POP7 nuclear RNase P subunit YBR257W POP4 mitochondrial matrix [T] POP4 involved in processing of tRNAs and rRNAs YDL119C mitochondrial inner membrane [O] YDL119c similarity to bovine Graves disease carrier protein YDR044W HEM13 mitochondrial inner membrane [M] HEM13 coproporphyrinogen III oxidase YDR350C TCM10 mitochondria [U] TCM10 hypothetical protein YDR478W SNM1 mitochondrial matrix [T] SNM1 RNA binding protein of RNase MRP YGL064C mitochondria [U] YGL064c similarity to YLR276c and YKR024c YGL136C mitochondria [U] YGL136c weak similarity to E.coli ftsJ protein YGR030C POP6 mitochondrial matrix [T] POP6 required for processing of tRNAs and rRNAs YGR096W mitochondrial inner membrane [O] YGR096w hypothetical mitochondrial transport protein YGR101W mitochondrial inner membrane [U] YGR101w weak similarity to B.subtilis YqgP YGR169C mitochondria [M] YGR169c similarity to RIB2P YGR255C COQ6 mitochondria [M] COQ6 monooxygenase YGR257C mitochondrial inner membrane [O] YGR257c similarity to C.elegans C16C10.1 YHR002W mitochondrial inner membrane [A] YHR002w similarity to bovine mitochondrial carrier protein/Grave's disease carrier protein YHR062C RPP1 mitochondrial matrix [T] RPP1 required for processing of tRNA and 35S rRNA YHR086W NAM8 mitochondria [T] NAM8 meiotic recombination protein YIL006W mitochondrial inner membrane [A] YIL006w similarity to FLX1P YKL114C APN1 mitochondria [D] APN1 AP endonuclease YKL155C RSM22 mitochondrial matrix [U] RSM22 similarity to S. pombe SPAC1420.04c putative cytochrome c oxidase assembly protein YLL018C-A COX19 mitochondrial intermembrane space [U] COX19 similarity to hypothetical S. pombe protein (YEB7) YLR164W mitochondrial inner membrane [E] YLR164w strong similarity to SDH4P YLR165C PUS5 mitochondria [M] PUS5 RNA:pseudouridine (Psi)-synthase YML060W OGG1 mitochondria [D] OGG1 8-oxoguanine DNA glycosylase YMR038C LYS7 mitochondrial intermembrane space [F] LYS7 copper chaperone for superoxide dismutase SOD1P YMR061W RNA14 mitochondria [T] RNA14 component of pre-mRNA 3'-end processing factor CF I YMR166C mitochondrial inner membrane [O] YMR166c similarity to members of the mitochondrial carrier protein family YMR188C mitochondrial matrix [P] YMR188c weak similarity to bacterial ribosomal protein S17 YNL066W SUN4 mitochondrial matrix [M] SUN4 strong similarity to YIL123w, UTH1P, NCA3P and C. wickerhamii beta-glucosidase protein YNL081C mitochondrial matrix [P] YNL081c similarity to ribosomal protein S13 YNL083W mitochondrial inner membrane [O] YNL083w weak similarity to rabbit peroxisomal Ca-dependent solute carrier YNL221C POP1 mitochondrial matrix [T] POP1 protein component of ribonuclease P and ribonuclease MRP YNL282W POP3 mitochondrial matrix [T] POP3 involved in processsing of tRNAs and rRNAs YNL292W PUS4 mitochondria [T] PUS4 pseudouridine synthase YOR241W MET7 mitochondria [M] MET7 tetrahydrofolylpolyglutamate synthase YOR274W MOD5 mitochondria [T] MOD5 tRNA isopentenyltransferase YPL183W-A mitochondrial matrix [P] YPL183w-a strong similarity to mitochondrial and bacterial ribosomal L36 proteins YPR021C mitochondrial inner membrane [A] YPR021c similarity to human citrate transporter protein